Table 2 Ophthalmologic findings of Erdheim-Chester disease
From: Erdheim-Chester disease with bilateral orbital masses and multi-systemic symptoms: two case reports
Eye involvement | Characteristic features | Radiological findings |
|---|---|---|
Palpebrae | Xanthelasmas | Hypointense on MRI [9] |
Orbit | Progressive bilateral proptosis [3] | Hypodensity on CT and isointensity to hypointensity on MRI with heterogeneous enhancement [10] |
 Optic nerve | Decreased visual acuity [3] | Enhancement or compression of the optic nerve on MRI [11] |
 Extraocular muscle | Ophthalmoplegia [3] | Enhancement or enlargement of the muscle on MRI [11] |
Intraocular | ||
 Anterior chamber | Uveitis (cells) | —— |
 Vitreous | Vitritis | —— |
 Retina | Recurrent Serous Retinal Detachment [12] | Drusen-like deposits of histiocytic material with progressive staining on fluorescein angiography [12] |
 Optic disc | Oedema [11] | —— |
 RPE | Chronic pigmentary and atrophic changes along with pigment clumping [12] | —— |
 Choroid | Quiescent choroidal neovascularization [13] | Disappearance of intermediate and large choroidal vessels and intact choriocapillaris in the lesion on EDI-OCT [14] |