Number | Author [ref.] | Gender/ age | Presentation | Tumor location | Tumor size (cm) | Liver invasion | Metastasis | Other component | Treatments | Prognosis, follow-up (month) |
---|---|---|---|---|---|---|---|---|---|---|
1 | Papotti et al. [3] | M/50 | Unclear | Unclear | <1 | - | - | AC | Cho | DFS, 12 |
2 | Papotti et al. [3] | M/65 | Unclear | Fundus | 2.5 | - | Liver | - | Cho | Died, 14 |
3 | Jun et al. [4] | M/55 | AP, jaundice | Unclear | Unclear | Unclear | Lymph node | - | Needle biopsy, Che | Died, 1 |
4 | Jun et al. [4] | F/67 | AP | Unclear | Huge | + | Lymph node | - | Needle biopsy, Che | Died, 10 |
5 | Noske and Pahl [5] | F/81 | AP, jaundice | Neck | 5 | + | Bone | Adenosquamous | Palliative surgery | Unknown |
6 | Oshiro et al. [6] | F/55 | Back pain, fever | Body | 4.9 | - | - | AC, SCNEC | Radical Cho | DFS, 20 |
7 | Shimono et al. [7] | F/64 | AP | Unclear | 11.5 | + | - | - | Che, Rad, extended hepatectomy | DFS, 36 |
8 | Iype et al. [8] | M/85 | Anorexia, weight loss | Fundus | 1.5 | - | Unclear | AC | Cho, Che | Died, 21 |
9 | Lin et al. [9] | F/65 | Cushing’s syndrome | Body | Unclear | - | - | -(ACTH-producing) | Radical Cho, Che | Died, 2 |
10 | Sato et al. [10] | F/68 | Negative | Fundus | 3 | + | Lymph node | AC | Cho, extended hepatectomy | DFS, 12 |
11 | Paniz et al. [11] | F/48 | AP | Fundus | 3.5 | + | Unclear | AC | Cho, extended hepatectomy | Unknown |
12 | Al-Brahim and Albannai [12] | M/45 | AP, jaundice | Fundus | 5.7 | + | Unclear | AC | Cho, Che | Unknown |
13 | Okuyam et al. [13] | M/64 | Abdominal fullness | Fundus | 2.5 | + | Lymph node | - | Biopsy, Che | Died, 22 |
14 | Nakagawa et al. [14] | M/56 | Exophthalmos | Unclear | 9 | + | Multiple | AC | Che, Rad | Died, 36 |
15 | Meguro et al. [15] | F/54 | Negative | Unclear | Unclear | - | - | AC | Cho, extrahepatic bile duct resection | DFS, 24 |
16 | Russo et al. [16] | M/59 | AP | Body | 4 | + | Lymph node | Mucinous carcinoma | Radical Cho | Unknown |
17 | Current study, 2014 | F/63 | AP, fever | Body | 2.0 | - | - | AC | Radical Cho | DFS, 12 |