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Table 1 Cases of MFH/UPS in the colorectum and anus

From: Surgical management of primary undifferentiated pleomorphic sarcoma of the rectum: a case report and review of the literature

Author

Age

Sex

Site

Size (cm)

Symptom

Primary treatment

Adjuvant

Recurrence

Prognosis (month)

Verma P. 1979 [21]

38

M

Rectum

12

Abdominal pain

Surgery (laparotomy)

No

No

Alive 14 M

Sewell R. 1980 [22]

74

M

Transverse

8.5 × 5 ×5

Anorexia, diarrhea

Surgery (laparotomy)

No

No

Alive 12 M

Levinson M. M. 1981 [23]

17

M

Transverse, rectosigmoid

10, 8.3 × 2

Abdominal pain, fever

Surgery (laparotomy)

No

ND

ND

Waxman M. 1983 [24]

52

F

Sigmoid

7.5 × 6

Abdominal pain

Surgery (laparotomy)

No

Yes (local)

Dead 9M

Rubbini M. 1983 [25]

60

M

Sigmoid

7

Bloody stool

Surgery (laparotomy)

Chemotherapy

Yes (liver, lymph node)

Dead 26 M

Spagnoli L. G. 1984 [26]

52

F

Anorectal

2.6 × 1.6 × 1

Bloody stool

Surgery (laparotomy)

No

Yes (lung, local)

Dead 24 M

Kukora J. S. 1985 [27]

73

M

Transverse

2.5 × 2

Abdominal pain, constipation

Surgery (laparotomy)

ND

No

Alive 48 M

Baratz M. 1986 [28]

73

M

Transverse

15 × 7 × 4, 8 × 4 × 1

Anorexia, anemia

Surgery (laparotomy)

No

No

Alive 6 M

Satake T. 1988 [29]

62

M

Ascending, transverse

17 × 10 × 8, 19 × 7 × 7

Abdominal mass

No (autopsy)

ND

ND

ND

Flood H. D. 1989 [30]

41

M

Anal canal

6

Abdominal mass

Surgery (laparotomy)

Radiotherapy

No

Alive 16 M

Katz R. N. 1990 [31]

62

F

Cecum

2 × 1.8 × 1.1

Abdominal pain

Surgery (laparotomy)

No

No

Alive 3 M

Murata I. 1993 [32]

50

M

Ascending

9.65 × 6.0 × 5.0

Abdominal distention, anorexia

Surgery (laparotomy)

Chemotherapy

No

Alive 10 M

Huang Z. 1993 [33]

12

M

Ascending

3.5

Abdominal pain

Surgery (laparotomy)

No

No

Alive 16 M

Makino M. 1994 [34]

72

M

Transverse

7.5 × 5.0

Abdominal pain

Surgery (laparotomy)

No

Yes (peritoneum)

Dead 4 M

Hiraoka N. 1997 [35]

64

M

Cecum

4 × 5 × 3

Abdominal distention

Surgery (laparotomy)

Chemotherapy

Yes (lymph node)

Dead 4 M

Kawashima H. 1997 [36]

50

F

Descending

4 × 3.2

Abdominal pain, diarrhea

Surgery (laparotomy)

No

No

Alive 84 M

Udaka T. 1999 [37]

47

M

Ascending

7 × 5 × 4

Abdominal mass

Surgery (laparotomy)

No

No

Alive 13 M

Singh D. R. 1999 [38]

55

M

Rectum

4 × 2.5

Tenesmus, perineal pain

Surgery (laparotomy)

Chemoradiotherapy

No

Alive 46 M

Okubo H. 2005 [39]

66

M

Ascending

14.5 × 8.0 × 4.5

Abdominal pain

Surgery (laparotomy)

No

No

Alive 33 M

Gupta C. 2006 [40]

46

F

Cecum, ascending

17

Abdominal distention, anorexia

Surgery (laparotomy)

No

No

Alive 36 M

Fu D. L. 2007 [41]

70

M

Cecum

12 × 10

Abdominal pain

Surgery (laparotomy)

No

Yes (lung)

Dead 1 M

Bosmans B. 2007 [42]

73

M

Sigmoid

3.2

Anemia

Surgery (laparotomy)

No

No

Alive 22 M

Kim B. G. 2008 [43]

63

F

Anal canal

1.7 × 1.3 × 0.3

Bloody stool, anal mass

Surgery (TAE)

Radiotherapy

No

Alive 15 M

Azizi R. 2011 [44]

80

M

Rectum

5 × 4 × 2.5

Rectal bleeding

Surgery (laparotomy)

No

ND

ND

Wang YJ 2012 [45]

55

M

Sigmoid

6

Abdominal pain

Surgery (laparotomy)

No

Yes (local)

Dead 5 M

Ji W. 2016 [46]

68

F

Ascending

8 × 6

Fever

Surgery (laparotomy)

Radiotherapy

Yes (local)

Dead 60 M

Kazama 2019 [47]

50

M

Ascending

7.2 × 6.0

Abdominal pain, numbness

Surgery (laparotomy)

Chemotherapy

No

Alive 6 M

Han X. 2022 [48]

65

F

Descending

10 × 8 × 5

Fever, fatigue

Surgery (laparotomy)

No

No

Alive 12 M

Our case 2022

85

F

Rectum

11 × 8.3 × 3

Anal pain

Surgery (laparoscopy)

No

Yes (lymph node)

Alive 12 M

  1. MFH malignant fibrous histiocytoma, UPS undifferentiated pleomorphic sarcoma, ND not described