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Table 2 Neoplasic risk and age of onset

From: Cowden syndrome is a risk factor for multiple neoplasm: a case report

Tumor

Risk to life (%)

Beginning age

Breast

85

30

Thyroid

35

30-40

Kidney cells

34

50

Endometrium

28

40-50

Gastrointestinal

9

40

Melanoma

6

4

  1. Adapted from https://rarediseases.org/rare-diseases/pten-hamartoma-tumor-syndrome/Copyright©2019