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Table 1 Classification of PEComas proposed by Folpe et al

From: A rare case of perivascular epithelioid cell tumor (PEComa) of the greater omentum

 

Benign

Uncertain malignant potential

Malignant

Criteria

No worrisome features

Nuclear pleomorphism/multinucleated giant cells only

Two or more worrisome features

 

Size < 5 cm

or

Size > 5 cm

 

Non-infiltrative

Size > 5 cm only

Infiltrative

 

Non-high nuclear grade and cellularity

 

High nuclear grade and cellularity

 

Mitotic rate  1/50HPF

 

Mitotic rate  1/50HPF

 

No necrosis

 

Necrosis

 

No vascular invasion

 

Vascular invasion