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Table 2 Hereditary Forms of Pheochromocytoma.

From: Pheochromocytoma associated with neurofibromatosis type 1: concepts and current trends

Syndrome Frequency of Pheo (%) Gene Chromosome location
MEN type II 30-50 RET oncogene 10q11
VHL disease 15-20 VHL tumor suppressor gene 3p25
NF type 1 1-5 Neurofibromatosis type 1 17q11
Familial carotid body tumors   Paraganglioma 11q21-23