Table 2 Hereditary Forms of Pheochromocytoma.
From: Pheochromocytoma associated with neurofibromatosis type 1: concepts and current trends
Syndrome | Frequency of Pheo (%) | Gene | Chromosome location |
|---|---|---|---|
MEN type II | 30-50 | RET oncogene | 10q11 |
VHL disease | 15-20 | VHL tumor suppressor gene | 3p25 |
NF type 1 | 1-5 | Neurofibromatosis type 1 | 17q11 |
Familial carotid body tumors | Paraganglioma | 11q21-23 |