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Table 1 Data of the published literatures regarding splenic rupture secondary to splenic angiosarcoma

From: Spontaneous rupture of primary splenic angiosarcoma: a case report and literature review

Gender

Age

Clinical manifestations

Laboratory result

Early metastasis

Treatment

Prognosis

Reference

Female

45

Left upper abdominal pain and mass, shock

Anemia, thrombocytopenia

Early multiple metastases

Splenectomy and chemotherapy

Died 4 months after surgery

[6]

Female

79

None

Anemia

No

Splenectomy

Discharged on the 10th postoperative day

[7]

Female

17

Shock, left upper abdominal pain and mass

Anemia, thrombocytopenia

No

Splenectomy

Disease-free of 16 months

[8]

Female

45

Left upper abdominal pain

Thrombocytopenia

Liver metastases after 3 months

Splenectomy and chemotherapy

Died 7 months after surgery

[9]

Male

57

Upper abdominal pain, shock

Anemia, thrombocytopenia

Early liver metastases

Splenectomy

Died 1 day after surgery

[10]

Female

64

Fatigue, upper abdominal pain

Thrombocytopenia

Early bone metastases

Splenectomy and chemotherapy

Died 4 months after surgery

[11]

Male

76

Upper abdominal pain, shock

Anemia, thrombocytopenia

Peritoneal and liver metastases after 4 weeks

Splenectomy

Died 6 weeks after splenectomy

[12]

Female

37

Left upper abdominal pain

Anemia

Liver metastases

Splenectomy and chemotherapy

Died 6 months after surgery

[13]

Male

53

Upper abdominal pain, shock

Anemia, thrombocytopenia

Early liver metastases

Splenectomy

Died 7 months after surgery

[14]

Female

35

Upper abdominal pain, shock

None

Early liver metastases

Splenectomy

Died 4 day after surgery

[15]

Female

80 and over

Shock

Anemia

 

Splenectomy

 

[16]

Female

Middle age

  

Early liver metastases

Splenectomy

 

[17]